Presents in patients between 43 and 88, with a mean age of 67. 2,5,7,8,10,11,13,17,18
Other groups with higher incidences are First Nation Peoples in Canada, Punjabis, and Native Americans. 5,8,10,13,17
While the etiology of ALect2 is unknown and there is currently no effective treatment, it is important to avoid misdiagnosis. Applying ineffective treatment may be harmful. Regrettably, in one series 4 patients had received chemotherapy consequent to an erroneous diagnosis of AL.14